The French national registry of primary immunodeficiency diseases

CEREDIH: The French PID Study Group - Clinical Immunology, 2010 - Elsevier
The French National Reference Center of Primary Immunodeficiencies (CEREDIH) was
established in 2005 and now constitutes a nationwide network of pediatric and adult
medicine departments in university medical centers. The registry comprises a total of 3,083
patients (mainly children), with an overall prevalence of 4.4 cases per 100,000 inhabitants.
Predominantly B-cell immunodeficiencies are the most common diseases observed (43%).
The proportion of common variable immunodeficiencies (CVIDs, 14%) is lower than reported …